acoustic neuroma

DEFINITION

Acoustic neuroma is an uncommon, noncancerous (benign) and usually slow-growing tumor that develops on the main nerve leading from your inner ear to your brain. Because branches of this nerve directly influence your balance and hearing, pressure from an acoustic neuroma can cause hearing loss, ringing in your ear and unsteadiness.

Also known as vestibular schwannoma, acoustic neuroma usually grows slowly or not at all. However, in a few cases, it may grow rapidly and become large enough to press against the brain and interfere with vital functions.

Treatments for acoustic neuroma include regular monitoring, radiation and surgical removal.

CAUSES

The cause of acoustic neuromas — tumors on the main balance nerves leading from your inner ear to your brain (eighth cranial nerve) — appears to be a malfunctioning gene on chromosome 22. Normally, this gene produces a protein that helps control the growth of Schwann cells covering the nerves. What makes this gene malfunction isn’t clear, and currently there are no known risk factors for getting an acoustic neuroma.

Scientists do know the faulty gene is inherited in neurofibromatosis type 2, a rare disorder that usually involves the growth of tumors on balance nerves on both sides of your head (bilateral vestibular schwannomas).

SYMPTOMS

The signs and symptoms of acoustic neuroma develop from direct effects on the main nerve or from the tumor pressing on adjacent nerves, nearby blood vessels or brain structures.

As the tumor grows, it may be more likely to cause signs and symptoms, although tumor size doesn’t always determine effects. It’s possible for a small tumor to cause significant signs and symptoms.

You may experience signs and symptoms such as:

  • Hearing loss, usually gradual — although in some cases sudden — and occurring on only one side or more pronounced on one side
  • Ringing (tinnitus) in the affected ear
  • Unsteadiness, loss of balance
  • Dizziness (vertigo)
  • Facial numbness and very rarely, weakness
  • In rare cases, an acoustic neuroma may grow large enough to compress the brainstem and threaten your life.


When to see your doctor

  • See your doctor if you notice hearing loss in one ear, ringing in your ear or trouble with your balance. Early diagnosis of an acoustic neuroma may help keep the tumor from growing large enough to cause serious consequences, such as total hearing loss or a life-threatening buildup of fluid within your skull.